中国肝豆状核变性诊疗临床指南：药物治疗与外科干预的结合《中国肝豆状核变性诊疗临床指南：药物治疗与外科干预的结合》制订组

Chinese clinical guidelines for the diagnosis and treatment of hepatolenticular degeneration: The combination of pharmacotherapy and surgical intervention

摘要:

为帮助包括肝移植、神经内科、消化内科等相关临床医师在肝豆状核变性（HLD）肝移植手术中做出合理决策及建议，该临床指南制订组牵头组织国内相关领域专家，以HLD及肝移植手术的临床和基础研究进展为依据，共同编写了《中国肝豆状核变性诊疗临床指南：药物治疗与外科干预的结合》。内容包括HLD的临床表现、诊断、肝移植外科干预与药物治疗及相关预后。

Abstract:

In order to help relevant clinical physicians from liver transplantation， neurology， gastroenterology， and other departments to make reasonable decisions and suggestions during liver transplantation for hepatolenticular degeneration （HLD）， the work group of the guidelines organized the Chinese experts in related fields to jointly develop Chinese clinical guidelines for the diagnosis and treatment of hepatolenticular degeneration： The combination of pharmacotherapy and surgical intervention. The guidelines elaborate on the clinical manifestations， diagnosis， surgical intervention and pharmacotherapy for liver transplantation， and prognosis of HLD. ［Journal of International Neurology and Neurosurgery, 2024, 51(5): 1-13］